JCCVS

Journal of Cardiology & Cardiovascular Surgery scientific, open-access, double-blind peer-reviewed journal covering a wide spectrum of topics in cardiology and cardiovascular surgery.

EndNote Style
Index
Case Report
Total anomalous pulmonary venous connection: mixed variation [2(1/2) + 1(1/2)] type: Bizarre Pattern: a case report
Among all variants of total anomalous pulmonary venous connection, mixed variety is a rare congenital anomaly. It comprises 3 different patterns including 2+2, 3+1, bizarre variations. These bizarre variations are uncommon findings in mixed variety. In this particular case, we report surgical correction of such rare variation comprising [2(1/2) cardiac + 1(1/2) supracardiac] type of pulmonary venous drainage. These variations impose the importance of preoperative delineation of heterogeneous venous drainage and subsequent planning for surgical repair.


1. Delius RE, de Leval MR, Elliott WJ, Stark J. Mixed total pulmonary venous drainage: still a surgical challenge. J Thorac Cardiovasc Surg. 1996;112(6):1581-1588. doi:10.1016/S0022-5223(96)70017-X
2. Darling RC, Rothney WB, Craig JM. Total pulmonary venous drainage into the right side of the heart: report of 17 autopsied cases not associated with other major cardiovascular anomalies. Lab Invest. 1957; 6(1):44-64.
3. Chowdhury UK, Malhotra A, Kothari SS, et al. A suggested new surgical classification for mixed totally anomalous pulmonary venous connection. Cardiol Young. 2007;17(4):342-353. doi:10.1017/S 104795110700073X
4. Yong MS, Shann F, d’Udekem Y, et al. Hemodynamic index for risk stratification after neonatal total anomalous pulmonary venous drainage repair.Ann Thorac Surg. 2012;94(5):1584-1587. doi:10.1016/j.athoracsur.2012.06.013
5. Sengupta A, Gauvreau K, Kaza A, et al. A risk prediction model for reintervention after total anomalous pulmonary venous connection repair. Ann Thorac Surg. 2023;116(4):796-802. doi:10.1016/j.athoracsur. 2022.05.058
6. Hellenkamp K, Unsöld B, Mushemi-Blake S, et al. Echocardiographic estimation of mean pulmonary artery pressure: a comparison of different approaches to assign the likelihood of pulmonary hypertension. J Am Soc Echocardiogr. 2018;31(1):89-98. doi:10.1016/j.echo.2017.09.009
7. Matsuhisa H, Oshima Y, Higuma T, et al. Computed tomography-based surgical strategy for total anomalous pulmonary venous connection. Eur J Cardiothorac Surg. 2020;58(2):237-245. doi:10.1093/ejcts/ezaa028
8. Vanderlaan RD, Caldarone CA. Surgical approaches to total anomalous pulmonary venous connection.Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu. 2018;21:83-91. doi:10.1053/j.pcsu.2017.11.010
9. Chowdhury UK, Airan B, Malhotra A, et al. Mixed total anomalous pulmonary venous connection: anatomic variations, surgical approach, techniques, and results.J Thorac Cardiovasc Surg. 2008;135(1):106-116.e1165. doi:10.1016/j.jtcvs.2007.08.028
10. Wen C, Shi G, Zhang Q, et al. Review of surgical experience in 61 patients with mixed total anomalous pulmonary venous connection. Eur J Cardiothorac Surg. 2022;62(2):ezac217. doi:10.1093/ejcts/ezac217
Volume 3, Issue 3, 2025
Page : 65-67
_Footer